Аннотация:Ever since 1938, when Schaltenbrand first described spontaneous intracranial hypotension (SIH), which he termed spontaneous aliquorrhea,1 clinicians have recognized the disorder by its clinical resemblance to post lumbar puncture symptoms. However, SIH was thought to be rare until its associated MRI abnormalities were recognized in the early 1990s. These revolutionized the diagnosis of SIH and demonstrated that the disorder is by no means rare.2-4⇓⇓ Furthermore, the clinical and imaging spectrums are far broader than had been originally appreciated. Although Schaltenbrand believed the cause of the disorder was low production of the CSF, the overwhelming majority if not all cases of SIH result from spontaneous CSF leaks.
These leaks are typically at the level of the spine, particularly the thoracic spine and cervicothoracic junction, and only rarely at the skull base. Single or multiple meningeal diverticula are frequent and a minority of patients with SIH have evidence of a connective tissue disorder.4 The common clinical features …